<http://identifiers.org/uniprot/P55809> <http://www.w3.org/1999/02/22-rdf-syntax-ns#type> <http://www.biopax.org/release/biopax-level3.owl#ProteinReference> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#comment> "FUNCTION: Key enzyme for ketone body catabolism. Transfers the CoA moiety from succinate to acetoacetate. Formation of the enzyme-CoA intermediate proceeds via an unstable anhydride species formed between the carboxylate groups of the enzyme and substrate. CATALYTIC ACTIVITY: Succinyl-CoA + a 3-oxo acid = succinate + a 3- oxoacyl-CoA. PATHWAY: Ketone metabolism; succinyl-CoA degradation; acetoacetyl- CoA from succinyl-CoA: step 1/1. SUBUNIT: Homodimer. SUBCELLULAR LOCATION: Mitochondrion matrix. TISSUE SPECIFICITY: Abundant in heart, followed in order by kidney, brain, and muscle, whereas in liver it is undetectable; also detectable in leukocytes and fibroblasts. DISEASE: Defects in OXCT1 are a cause of succinyl-CoA-3-ketoacid- CoA transferase deficiency (SCOTD) [MIM:245050]. A disorder of ketone body metabolism, characterized by episodic ketoacidosis. Patients are usually asymptomatic between episodes. SIMILARITY: Belongs to the 3-oxoacid CoA-transferase family. WEB RESOURCE: Name=GeneReviews; URL=\"http://www.ncbi.nlm.nih.gov/sites/GeneTests/lab/gene/OXCT1\"; GENE SYNONYMS:OXCT1 OXCT SCOT. COPYRIGHT: Protein annotation is derived from the UniProt Consortium (http://www.uniprot.org/). Distributed under the Creative Commons Attribution-NoDerivs License."^^<http://www.w3.org/2001/XMLSchema#string> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#comment> "SEQUENCE 520 AA; 56158 MW; 54DA790FB8EDA546 CRC64;"^^<http://www.w3.org/2001/XMLSchema#string> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#xref> <urn:biopax:RelationshipXref:NCBI+GENE_5019> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#xref> <urn:biopax:RelationshipXref:HGNC_HGNC%3A8527> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#xref> <urn:biopax:UnificationXref:UNIPROT_P55809> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#xref> <urn:biopax:RelationshipXref:REFSEQ_NP_000427> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#displayName> "SCOT1_HUMAN"^^<http://www.w3.org/2001/XMLSchema#string> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#name> "2.8.3.5"^^<http://www.w3.org/2001/XMLSchema#string> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#name> "3-oxoacid CoA-transferase 1"^^<http://www.w3.org/2001/XMLSchema#string> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#name> "Somatic-type succinyl-CoA:3-oxoacid CoA-transferase"^^<http://www.w3.org/2001/XMLSchema#string> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#name> "OXCT1"^^<http://www.w3.org/2001/XMLSchema#string> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#name> "SCOT-s"^^<http://www.w3.org/2001/XMLSchema#string> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#organism> <http://identifiers.org/taxonomy/9606> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#sequence> "MAALKLLSSGLRLCASARGSGATWYKGCVCSFSTSAHRHTKFYTDPVEAVKDIPDGATVLVGGFGLCGIPENLIDALLKTGVKGLTAVSNNAGVDNFGLGLLLRSKQIKRMVSSYVGENAEFERQYLSGELEVELTPQGTLAERIRAGGAGVPAFYTPTGYGTLVQEGGSPIKYNKDGSVAIASKPREVREFNGQHFILEEAITGDFALVKAWKADRAGNVIFRKSARNFNLPMCKAAETTVVEVEEIVDIGAFAPEDIHIPQIYVHRLIKGEKYEKRIERLSIRKEGDGEAKSAKPGDDVRERIIKRAALEFEDGMYANLGIGIPLLASNFISPNITVHLQSENGVLGLGPYPRQHEADADLINAGKETVTILPGASFFSSDESFAMIRGGHVDLTMLGAMQVSKYGDLANWMIPGKMVKGMGGAMDLVSSAKTKVVVTMEHSAKGNAHKIMEKCTLPLTGKQCVNRIITEKAVFDVDKKKGLTLIELWEGLTVDDVQKSTGCDFAVSPKLMPMQQIAN"^^<http://www.w3.org/2001/XMLSchema#string> .
<http://identifiers.org/uniprot/P55809> <http://www.biopax.org/release/biopax-level3.owl#standardName> "Succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial"^^<http://www.w3.org/2001/XMLSchema#string> .