Anaplastic Large Cell Lymphoma, ALK-Positive

Source:http://linkedlifedata.com/resource/umls/id/C1332079

Statements in which the resource exists.
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umls-concept:C1332079skos:definitionNCI: A T-cell peripheral lymphoma composed of usually large, pleomorphic, CD30 positive T-lymphocytes with abundant cytoplasm characterized by the presence of a translocation involving the ALK gene and expression of ALK fusion protein. Most patients present with peripheral and/or abdominal lymphadenopathy, and often have advanced disease and extranodal involvement.lld:umls
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