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| Predicate | Object |
|---|---|
| rdf:type | |
| lifeskim:mentions | |
| pubmed:issue |
2
|
| pubmed:dateCreated |
1992-6-2
|
| pubmed:abstractText |
In 24 subjects presenting with apparently idiopathic ventricular arrhythmias, a final diagnosis of arrhythmogenic right ventricular cardiomyopathy was formulated following global evaluation of the clinical, cross-sectional echocardiography and angiographic findings, and the observation of myocardial atrophy with fibrous-fatty substitution in right ventricular endomyocardial biopsy. All patients had good effort tolerance, and a normal cardiac silhouette. Ventricular arrhythmias with a left bundle branch block pattern were present in 23 cases (sustained ventricular tachycardia, nonsustained ventricular tachycardia, ventricular couplets, and ventricular premature complexes); 1 patient experienced an episode of ventricular fibrillation. A nearly constant electrocardiographic feature was T wave negativity in the right precordial leads. Cross-sectional echocardiography and hemodynamic studies showed that right ventricular impairment consisted only of localized structural and dynamic abnormalities; in a few cases the left ventricle was segmentally involved. Familial occurrence was present in 29% of the cases. No case of sudden death was observed during follow-up. These findings confirm that the concealed form of arrhythmogenic right ventricular cardiomyopathy is a cause of so-called "idiopathic" ventricular arrhythmias in subjects with apparently "normal hearts". Echocardiographic and angiographic investigations may lead to the correct diagnosis.
|
| pubmed:language |
eng
|
| pubmed:journal | |
| pubmed:citationSubset |
IM
|
| pubmed:status |
MEDLINE
|
| pubmed:month |
May
|
| pubmed:issn |
0167-5273
|
| pubmed:author | |
| pubmed:issnType |
Print
|
| pubmed:volume |
35
|
| pubmed:owner |
NLM
|
| pubmed:authorsComplete |
Y
|
| pubmed:pagination |
195-206; discussion 207-9
|
| pubmed:dateRevised |
2007-11-15
|
| pubmed:meshHeading |
pubmed-meshheading:1572740-Adolescent,
pubmed-meshheading:1572740-Adult,
pubmed-meshheading:1572740-Arrhythmias, Cardiac,
pubmed-meshheading:1572740-Bundle-Branch Block,
pubmed-meshheading:1572740-Cardiomyopathies,
pubmed-meshheading:1572740-Child,
pubmed-meshheading:1572740-Child, Preschool,
pubmed-meshheading:1572740-Coronary Angiography,
pubmed-meshheading:1572740-Echocardiography,
pubmed-meshheading:1572740-Electrocardiography,
pubmed-meshheading:1572740-Female,
pubmed-meshheading:1572740-Heart Catheterization,
pubmed-meshheading:1572740-Heart Ventricles,
pubmed-meshheading:1572740-Humans,
pubmed-meshheading:1572740-Male,
pubmed-meshheading:1572740-Middle Aged,
pubmed-meshheading:1572740-Myocardium,
pubmed-meshheading:1572740-Ventricular Fibrillation
|
| pubmed:year |
1992
|
| pubmed:articleTitle |
Clinical profile of concealed form of arrhythmogenic right ventricular cardiomyopathy presenting with apparently idiopathic ventricular arrhythmias.
|
| pubmed:affiliation |
Department of Cardiology, University of Padua Medical School, Italy.
|
| pubmed:publicationType |
Journal Article,
Research Support, Non-U.S. Gov't
|