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pubmed-article:10524651pubmed:abstractTextDesmoid tumours are histologically benign but due to their infiltration and compression of surrounding structures potentially life-threatening fibromatous lesions of unknown aetiology. The annual incidence rate is 2-4 per million people. The mesenteric variant constitutes about 10% of all desmoid tumours, although in familial adenomatous polyposis (FAP) patients this may be up to 70%. Due to the small number of patients with mesenteric desmoids the therapy is mainly empirical. This report describes the rationale as well as the value of the short- and long-term treatment (up to 6 years) with the anti-oestrogenic agent toremifene in combination with sulindac in two patients suffering from such a mesenteric desmoid tumour. These patients did not respond to sulindac alone and previous treatment with tamoxifen together with this non-steroidal anti-inflammatory drug had also failed. An overview of the literature on the management of these dismal tumours is presented.lld:pubmed
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pubmed-article:10524651pubmed:pagination1179-83lld:pubmed
pubmed-article:10524651pubmed:dateRevised2009-10-16lld:pubmed
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pubmed-article:10524651pubmed:articleTitleTreatment of mesenteric desmoid tumours with the anti-oestrogenic agent toremifene: case histories and an overview of the literature.lld:pubmed
pubmed-article:10524651pubmed:affiliationDepartment of Gastroenterology-Hepatology, Leiden University Medical Center, The Netherlands.lld:pubmed
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