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| Predicate | Object |
|---|---|
| rdf:type | |
| lifeskim:mentions | |
| pubmed:issue |
1
|
| pubmed:dateCreated |
1998-11-16
|
| pubmed:abstractText |
A case of non-cirrhotic portal fibrosis associated with pulmonary arteriovenous communication and pulmonary arterial hypertension is reported. The patient was a 7-year old boy who presented with hematemesis, cyanosis, hypoxemia and orthodeoxia. His liver pathology was compatible with non-cirrhotic portal fibrosis. His pulmonary angiography showed arteriovenous shunting and pulmonary arterial hypertension (mean pulmonary artery pressure 34 mmHg). His sister also had non-cirrhotic portal fibrosis with neither hypoxemia nor orthodeoxia. This report raises the possibility of non-cirrhotic portal fibrosis having a genetic etiology.
|
| pubmed:language |
eng
|
| pubmed:journal | |
| pubmed:citationSubset |
IM
|
| pubmed:status |
MEDLINE
|
| pubmed:month |
Mar
|
| pubmed:issn |
0125-1562
|
| pubmed:author | |
| pubmed:issnType |
Print
|
| pubmed:volume |
29
|
| pubmed:owner |
NLM
|
| pubmed:authorsComplete |
Y
|
| pubmed:pagination |
76-9
|
| pubmed:dateRevised |
2007-11-15
|
| pubmed:meshHeading |
pubmed-meshheading:9740273-Anoxia,
pubmed-meshheading:9740273-Child,
pubmed-meshheading:9740273-Family,
pubmed-meshheading:9740273-Hematemesis,
pubmed-meshheading:9740273-Humans,
pubmed-meshheading:9740273-Hypertension, Portal,
pubmed-meshheading:9740273-Hypertension, Pulmonary,
pubmed-meshheading:9740273-Liver,
pubmed-meshheading:9740273-Liver Cirrhosis,
pubmed-meshheading:9740273-Male,
pubmed-meshheading:9740273-Pedigree
|
| pubmed:year |
1998
|
| pubmed:articleTitle |
Non-cirrhotic portal fibrosis associated with pulmonary arteriovenous communication and pulmonary arterial hypertension.
|
| pubmed:affiliation |
Department of Pediatrics, Faculty of Medicine, Chulalongkorn University, Bangkok, Thailand.
|
| pubmed:publicationType |
Journal Article,
Case Reports,
Research Support, Non-U.S. Gov't
|