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pubmed-article:17666373pubmed:abstractTextThe hypereosinophilic syndrome (HES) may be associated with the fusion of the platelet derived growth factor receptor a (PDGFRalpha) gene with the FIP1L1 gene in chromosome 4 coding for a constitutively activated PDGFRalpha tyrosine kinase. These cases with FIP1L1-PDGFRalpha rearrangement have been reported to be very sensitive to the tyrosine kinase inhibitor imatinib mesylate.lld:pubmed
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pubmed-article:17666373pubmed:articleTitleThe efficacy of imatinib mesylate in patients with FIP1L1-PDGFRalpha-positive hypereosinophilic syndrome. Results of a multicenter prospective study.lld:pubmed
pubmed-article:17666373pubmed:affiliationDepartment of Hematology-Oncology L. and A. Seràgnoli, S.Orsola-Malpighi University Hospital, Bologna, Italy. michele.baccarani@unibo.itlld:pubmed
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